FBN1 antibody (clone 3H6), anti-human
€435.00
In stock
SKU
AC-AT2010a
Catalog Number: AC-AT2010a
Size: 100 µg
Isotype: mouse IgG2a Kappa
Applications: WB, IHC, E
Request Information AC-AT2010a">Request Information
Size: 100 µg
Isotype: mouse IgG2a Kappa
Applications: WB, IHC, E
Request Information AC-AT2010a">Request Information
Background:
This gene encodes a member of the fibrillin family. The encoded protein is a large, extracellular matrix glycoprotein that serve as a structural component of 10-12 nm calcium-binding microfibrils. These microfibrils provide force bearing structural support in elastic and nonelastic connective tissue throughout the body. Mutations in this gene are associated with Marfan syndrome, isolated ectopia lentis, autosomal dominant Weill-Marchesani syndrome, MASS syndrome, and Shprintzen-Goldberg craniosynostosis syndrome.
Other Names:
Fibrillin-1, FBN1, FBN
Antigen Type:
Recombinant Protein
Gene Name: FBN1 (HGNC:3603)
Gene ID: 2200
NCBI Accession: NP_000129.3
Primary Accession: P35555
Other Accession: NM_000138
Format: Clear, colorless solution in phosphate buffered saline, pH 7.2 .
This gene encodes a member of the fibrillin family. The encoded protein is a large, extracellular matrix glycoprotein that serve as a structural component of 10-12 nm calcium-binding microfibrils. These microfibrils provide force bearing structural support in elastic and nonelastic connective tissue throughout the body. Mutations in this gene are associated with Marfan syndrome, isolated ectopia lentis, autosomal dominant Weill-Marchesani syndrome, MASS syndrome, and Shprintzen-Goldberg craniosynostosis syndrome.
Other Names:
Fibrillin-1, FBN1, FBN
Antigen Type:
Recombinant Protein
Gene Name: FBN1 (HGNC:3603)
Gene ID: 2200
NCBI Accession: NP_000129.3
Primary Accession: P35555
Other Accession: NM_000138
Format: Clear, colorless solution in phosphate buffered saline, pH 7.2 .
| Is Featured? | No |
|---|
Write Your Own Review