GNS polyclonal (Center S298), anti-human
€0.00
In stock
SKU
AC-AP6574b
Catalog Number: AC-AP6574b
Size: 80 µl, 400 µl
Isotype: Rabbit IgG
Clone Name: RB19341
Applications: FC, IHC-P, WB
Datasheet
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Size: 80 µl, 400 µl
Isotype: Rabbit IgG
Clone Name: RB19341
Applications: FC, IHC-P, WB
Datasheet
Request Information
Background:
GNS is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.
Other Names:
N-acetylglucosamine-6-sulfatase, Glucosamine-6-sulfatase, G6S, GNS
Target/Specificity:
This GNS antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 283-313 amino acids from the Central region of human GNS.
Antigen Region:
283-313
Antigen Type: Synthetic Peptide
Gene Name: GNS
Gene ID: 2799
Primary Accession: P15586
NCBI Accession: NP_002067.1
Format: Purified polyclonal antibody supplied in PBS with 0.09% (W/V) sodium azide. This antibody is prepared by Saturated Ammonium Sulfate (SAS) precipitation followed by dialysis against PBS.
GNS is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.
Other Names:
N-acetylglucosamine-6-sulfatase, Glucosamine-6-sulfatase, G6S, GNS
Target/Specificity:
This GNS antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 283-313 amino acids from the Central region of human GNS.
Antigen Region:
283-313
Antigen Type: Synthetic Peptide
Gene Name: GNS
Gene ID: 2799
Primary Accession: P15586
NCBI Accession: NP_002067.1
Format: Purified polyclonal antibody supplied in PBS with 0.09% (W/V) sodium azide. This antibody is prepared by Saturated Ammonium Sulfate (SAS) precipitation followed by dialysis against PBS.
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