HADHA polyclonal, anti-human

Background:
This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.

Synonyms: ECHA, GBP, HADH, LCEH, LCHAD, MTPA, TP-ALPHA, trifunctional enzyme subunit alpha, mitochondrial

Cellular Location: Cytoplasm

Immunogen:
A synthetic peptide of human HADHA

Gene Symbol: HADHA

Gene ID: 3030

Swiss prot: P40939

Calculated MW: 83kDa

Recommended dilution:
IHC 1:50-200

Purity:
Affinity purification

Storage Buffer:
Buffer: PBS with 0.03% Proclin300, 50% glycerol, pH7.3.

Storage:
Store at -20℃. Avoid freeze / thaw cycles.