MCCC2 polyclonal, anti-human, mouse, rat

Background:
This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.

Synonyms: MCCB

Cellular Location: Mitochondrion matrix

Immunogen:
Recombinant protein of human MCCC2

Gene Symbol: MCCC2

Gene ID: 64087

Swiss prot: Q9HCC0

Calculated MW: 61kDa

Recommended dilution:
WB 1:500-2000, IHC 1:50-200,

Purity:
Affinity purification

Storage Buffer:
Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3.

Storage:
Store at -20℃. Avoid freeze / thaw cycles.