Nebulin (clone ), anti-human, mouse, rat, chicken, xenopus
€445.00
In stock
SKU
251776
Protein Family: Enzymes
Pathway and Disease: Signaling Molecules and Interaction
Description:
Nebulin is a large muscle protein involved in maintaining the structural integrity of sarcomeres and the membrane system associated with the myofibrils. Nebulin binds and stabilizes F-actin. Defects in nebulin are the cause of nemaline myopathy type 2 (NEM2). NEM2 is a form of nemaline myopathy. Nemaline myopathies are muscular disorders characterized by muscle weakness of varying severity and onset, and abnormal thread or rod-like structures in muscle fibers on histologic examination.
Alternate Names: Nebulin, NEB
Application Notes: E: 1:500-1:1,000; WB: 1:100-1:500
Accession No.: P20929
Antigen: Chicken breast nebulin.
Format: Each vial contains 0.1 mg IgG in 0.1 ml (1 mg/ml) of PBS pH7.4, 2% BSA with 0.09% sodium azide. Antibody was purified by Protein-G affinity chromatography.
Storage:
Store at -20°C. Minimize freeze-thaw cycles. Product is guaranteed one year from the date of shipment.
Pathway and Disease: Signaling Molecules and Interaction
Description:
Nebulin is a large muscle protein involved in maintaining the structural integrity of sarcomeres and the membrane system associated with the myofibrils. Nebulin binds and stabilizes F-actin. Defects in nebulin are the cause of nemaline myopathy type 2 (NEM2). NEM2 is a form of nemaline myopathy. Nemaline myopathies are muscular disorders characterized by muscle weakness of varying severity and onset, and abnormal thread or rod-like structures in muscle fibers on histologic examination.
Alternate Names: Nebulin, NEB
Application Notes: E: 1:500-1:1,000; WB: 1:100-1:500
Accession No.: P20929
Antigen: Chicken breast nebulin.
Format: Each vial contains 0.1 mg IgG in 0.1 ml (1 mg/ml) of PBS pH7.4, 2% BSA with 0.09% sodium azide. Antibody was purified by Protein-G affinity chromatography.
Storage:
Store at -20°C. Minimize freeze-thaw cycles. Product is guaranteed one year from the date of shipment.
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