PCCA polyclonal, anti-human, mouse, rat

Background:
The protein encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia. Multiple transcript variants encoding different isoforms have been found for this gene.

Synonyms: PCCA

Cellular Location: Mitochondrion matrix

Immunogen:
Recombinant protein of human PCCA

Gene Symbol: PCCA

Gene ID: 5095

Swiss prot: P05165

Calculated MW: 80kDa

Recommended dilution:
WB 1:1000-3000

Purity:
Affinity purification

Storage Buffer:
Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3.

Storage:
Store at -20℃. Avoid freeze / thaw cycles.