SGSH polyclonal, anti-human, mouse, rat
€388.00
In stock
SKU
BS71102
Background:
This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.
Alternative Name:
HSS, SFMD, MPS3A,
Application Dilution: WB: 1:500 - 1:2000, IHC: 1:50 - 1:200
Specificity: SGSH polyclonal antibody detects endogenous levels of SGSH protein.
Immunogen:
Recombinant protein of human SGSH.
MW: ~ 57 kDa
Swis Prot.: P51688
Purification & Purity:
The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen and the purity is > 95% (by SDS-PAGE).
Format:
1mg/ml in PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
Storage:
Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze-thaw cycles.
For research use only, not for use in diagnostic procedure.
This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.
Alternative Name:
HSS, SFMD, MPS3A,
Application Dilution: WB: 1:500 - 1:2000, IHC: 1:50 - 1:200
Specificity: SGSH polyclonal antibody detects endogenous levels of SGSH protein.
Immunogen:
Recombinant protein of human SGSH.
MW: ~ 57 kDa
Swis Prot.: P51688
Purification & Purity:
The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen and the purity is > 95% (by SDS-PAGE).
Format:
1mg/ml in PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
Storage:
Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze-thaw cycles.
For research use only, not for use in diagnostic procedure.
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